Giant Askin tumor: a diagnosis and therapeutic challenge.
نویسندگان
چکیده
In 1979, Askin and colleagues suggested a distinct clin icopathological entity, characterized by small round blue cell tumor ofthoracopulmonary region (Askin tumor), with varying degrees of neuronal differentiation 1 . Various designations have been used to describe this tumor, such as: adult neurob lastom a, peripheral neuroblastoma, peripheral neuroepithel iom a, primitive n euroectodermal tumor and Ewing’ s sarcoma family of tumors. Askin tumor is seen in children and adolescents with a 3:I female predominance. It is a highly malignant tumor with a very poor prognosis 2 . For advances to be made in treating these patients, therapy should be given in a multidisciplinary manner in the context of’ a clinical trial at a major medical centre that has expertise in managing such patients.
منابع مشابه
Malignant Small Round Cell Tumor Originating In The Thoracopulmonary Region " Askin Tumor "
SUMMARY Askin tumor is a peripheral neuroepithelioma originating in chest wall. It is a very aggressive tumor and with Ewing's sarcoma are the most frequent tumors of chest wall. The tumor is composed of small round or ovoid cells arranged in sheets with pseudorossette formation. Some times around vessels, glycogen staining is some times positive in H & E but always positive in E.M. In E.M be...
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عنوان ژورنال:
- JPMA. The Journal of the Pakistan Medical Association
دوره 52 2 شماره
صفحات -
تاریخ انتشار 2002